Treatment Strategies

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The most frequently associated orthopedic abnormalities involve the upper limbs and/or thumbs; Radial club hand/Radial agenesis are the conditions Dr.Paley frequently addresses in the VACTERL patient. Treatment strategies may incorporate re-orienting the wrist-hand angle (“ulnarization”), repositioning a finger to the position of a functioning thumb (“pollicization”), and, in the future, the possibility of forearm lengthening. For more information on these procedures, see Radial Club Hand.

Occasionally, lower limb deformities are also present, such as congenitally flexed knees (bony or soft tissue) and club foot (talipes). These issues are addressed on a case-to-case basis and may include correction with open surgeries and/or application of external fixators. Serial casting utilizing the techniques of Ignasio Ponseti are offered by our highly trained physical therapy team to address club foot pathology, if present. For more information on the Ponseti Method, see Clubfoot.

During the orthopedic treatment phase, we also keep a close watch on the child’s additional body system issues, and with the multi-disciplinary specialist available on-site at St. Mary’s hospital, can assure a high degree of safety. On site there is available pediatric cardiac surgery, intervention cardiac catheterization, a dedicated Pediatric Intensive Care Unit (PICU) team staffed with board-certified intensivists, pediatric ear, nose throat specialists, pediatric endocrinologists and general surgeons, and pulmonologists, amongst others. In the operating room, board-certified pediatric anesthesiologists attend our surgeries.